medsovetМедицинский СоветMeditsinskiy sovet = Medical Council2079-701X2658-5790REMEDIUM GROUP Ltd.10.21518/2079-701X-2019-8-48-53medsovet-2951Research ArticleАКТУАЛЬНОЕ В ОТОРИНОЛАРИНГОЛОГИИACTUAL IN OTORHINOLARYNGOLOGYОсобенности поражения лор-органов у взрослых пациентов с муковисцидозомFeatures of defeat of ent organs at adult patients with CFСвистушкинВ. М.SvistushkinV. M.

д.м.н., профессор, завкафедрой болезней уха, горла и носа Федерального государственного автономного образовательного учреждения высшего образования «Первый Московский государственный медицинский университет имени И.М. Сеченова» Министерства здравоохранения Российской Федерации (Сеченовский университет)

Dr. of Sci. (Med), Professor, Head of the Department of Ear, Throat and Nose Diseases, Federal State Autonomous Educational Institution of Higher Education «First Moscow State Medical University named after I.M. Sechenov», Ministry of Health of the Russian Federation (Sechenov University)

svvm3@yandex.ruСиньковЭ. В.SinkovE. V.

к.м.н., доцент кафедры болезней уха, горла и носа Федерального государственного автономного образовательного учреждения высшего образования «Первый Московский государственный медицинский университет имени И.М. Сеченова» Министерства здравоохранения Российской Федерации (Сеченовский университет)

Candidate of Medical Sciences, Associate Professor of the Department of Ear, Throat and Nose Diseases of the Federal State Autonomous Educational Institution of Higher Education «I.M. Sechenov First Moscow State Medical University» of the Ministry of Health of the Russian Federation (Sechenov University)

1178461@mail.ruШумковаГ. Л.ShumkovaG. L.

аспирант кафедры болезней уха, горла и носа Федерального государственного автономного образовательного учреждения высшего образования «Первый Московский государственный медицинский университет имени И.М. Сеченова» Министерства здравоохранения Российской Федерации (Сеченовский университет), научный сотрудник Центра муковисцидоза Федерального государственного бюджетного учреждения «Научноисследовательский институт пульмонологии Федерального медико-биологического агентства» на базе Государственного бюджетного учреждения здравоохранения города Москвы «Городская клиническая больница имени Д.Д. Плетнёва Департамента здравоохранения города Москвы»

Postgraduate student of the Department of Ear, Throat and Nose Diseases of the Federal State Autonomous Educational Institution of Higher Education of the First Sechenov Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University), Researcher at the Cystic Fibrosis Center of the Federal State Budgetary Institution «Research Institute of Pulmonology of the Federal Medical and Biological Agency» on the basis of the State Budgetary Institution of Healthcare of Moscow «D.D. Pletnev City Clinical Hospital of the Department of Healthcare of Moscow»

galina2212@yandex.ruАмелинаЕ. Л.AmelinaE. L.

к.м.н., зав. лабораторией муковисцидоза Федерального государственного бюджетного учреждения «Научно-исследовательский институт пульмонологии Федерального медико-биологического агентства»

Cand. of Sci. (Med.), Deputy Head of the Cystic Fibrosis Laboratory, the Federal State Budgetary Institution «Research Institute for Pulmonology of the Federal Medical Biological Agency»

eamelina@mail.ruКрасовскийС. А.KrasovskyS. A.

к.м.н., старший научный сотрудник лаборатории муковисцидоза Федерального государственного бюджетного учреждения «Научно-исследовательский институт пульмонологии Федерального медико-биологического агентства»; врач-пульмонолог 2-го пульмонологического отделения Государственного бюджетного учреждения здравоохранения города Москвы «Городская клиническая больница имени Д.Д. Плетнёва Департамента здравоохранения города Москвы»; старший научный сотрудник научно-клинического отдела муковисцидоза Федерального государственного бюджетного научного учреждения «Медико-генетический научный центр»

Cand. of Sci. (Med.), Senior Researcher, the Cystic Fibrosis Laboratory, the Federal State Budgetary Institution «Research Institute for Pulmonology of the Federal Medical Biological Agency»; a pulmonologyst, the 2nd Pulmonology Department of the State Budgetary Institution of Healthcare of the city of Moscow «Pletnev City Clinical Hospital of the Department of Health of Moscow»; Senior Researcher, the Research Clinical Cystic Fibrosis Department, the Federal State Budgetary Research Institution «Medical Genetic Research Center»

sa_krasovsky@mail.ruФедеральное государственное автономное образовательное учреждение высшего образования «Первый Московский государственный медицинский университет имени И.М. Сеченова» Министерства здравоохранения Российской Федерации (Сеченовский университет)РоссияFederal State Autonomous Educational Institution of Higher Education First Moscow State Medical University named after I.M. Sechenov of the Ministry of Health of the Russian Federation (Sechenov University)Russian FederationФедеральное государственное бюджетное учреждение «Научно-исследовательский институт пульмонологии Федерального медикобиологического агентства»РоссияFederal State Budgetary Institution «Research Institute for Pulmonology of the Federal Medical Biological Agency»Russian Federation201918042019084853Copyright © Свистушкин В.М., Синьков Э.В., Шумкова Г.Л., Амелина Е.Л., Красовский С.А., 20192019Свистушкин В.М., Синьков Э.В., Шумкова Г.Л., Амелина Е.Л., Красовский С.А.Svistushkin V.M., Sinkov E.V., Shumkova G.L., Amelina E.L., Krasovsky S.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.med-sovet.pro/jour/article/view/2951

Среди заболеваний ЛОР-органов у пациентов с муковисцидозом превалирует полипозный риносинусит. Застой инфицированной густой слизи в околоносовых пазухах и нарушение носового дыхания усугубляет тяжесть течения бронхолегочной патологии. Необходимо своевременное обследование и лечение патологии верхних дыхательных путей у пациентов с МВ. В хирургическом лечении методом выбора является расширенная FESS. Эта методика позволяет сохранить анатомию лицевого скелета и обеспечить дренаж околоносовых пазух. Наблюдение ЛОР-врачом и консервативное лечение полипозного риносинусита должно проводится в течение всей жизни пациента с МВ. Необходимо постоянное использование местной муколитической и антибактериальной терапии. Методом доставки лекарственных средств может служить компрессорный ингалятор с режимом для околоносовых пазух.

Among diseases of ENT organs at patients with the CF prevails chronic rhinosinusitis. Stagnation of the infected dense slime in the paranasal sinus and violation of nasal breath aggravates weight of a course of lung pathology. Timely inspection and treatment of pathology of the top airways at patients with CF is necessary. In surgical treatment method of a choice is expanded FESS. This technique allows to keep anatomy of a facial skeleton and to provide a drainage the paranasal sinus. Supervision by the ENT specialist and conservative treatment of a chronic rhinosinusitis has to is carried out during all life of the patient with CF. Continuous use of local mukolitichesky and antibacterial therapy is necessary. As method of delivery of medicines the compressor inhaler with the mode for the chronic rhinosinusitis can serve.

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The authors declare that there are no conflicts of interest present.