medsovetМедицинский СоветMeditsinskiy sovet = Medical Council2079-701X2658-5790REMEDIUM GROUP Ltd.10.21518/2079-701X-2022-16-8-150-159medsovet-6882Research ArticleДИССЕРТАНТDISSERTANTОпухоль эндолимфатического мешка: обзор литературыEndolymphatic sac tumor: rewiev of literaturehttps://orcid.org/0000-0001-5337-3239ДиабХ.М.А.DiabKh.M.A.

Диаб Хассан Мохамад Али, д.м.н., профессор, заместитель директора

123182, Москва, Волоколамское шоссе, д. 30, корп. 2

Hassan Mohamad Ali Diab, Dr. Sci. (Med.), Professor, Аssociate Director

30, Bldg. 2, Volokolamskoe Shosse, Moscow, 123182

hasandiab@mail.ruhttps://orcid.org/0000-0001-5636-5082ДайхесН. А.DaikhesN. A.

Дайхес Николай Аркадьевич,чл.- корр. РАН, д.м.н., профессор, главный внештатный оториноларинголог РФ, директор

123182, Москва, Волоколамское шоссе, д. 30, корп. 2

Nikolai A. Daikhes, Сorr. Member RAS, Dr. Sci. (Med.), Рrofessor, Director

30, Bldg. 2, Volokolamskoe Shosse, Moscow, 123182

otolar@fmbamail.ruhttps://orcid.org/0000-0003-0644-0528СайдулаевВ. А.SaydulaevV. А.

Сайдулаев Вахарсолта Алиевич, к.м.н., старший научный сотрудник отдела патологии уха и основания черепа

123182, Москва, Волоколамское шоссе, д. 30, корп. 2

Vakharsolta Saydulaev Saydulaev, Cand. Sci. (Med.), Senior Researcher of the Department of Pathology of the Ear and the Base of the Skull

30, Bldg. 2, Volokolamskoe Shosse, Moscow, 123182

sultan070487@mail.ruhttps://orcid.org/0000-0001-7864-5608ЮнусовА. С.YunusovA. S.

Юнусов Аднан Султанович, д.м.н., профессор, заместитель директора, руководитель научно-к линического отдела детской лор-патологии

123182, Москва, Волоколамское шоссе, д. 30, корп. 2

Adnan S. Yunusov, Dr. Sci. (Med.), Professor, Аssociate Director, Head of the Scientific and Clinical Department of Pediatric ENT Pathology

30, Bldg. 2, Volokolamskoe Shosse, Moscow, 123182

doctoradnan@mail.ruhttps://orcid.org/0000-0002-7188-3280ПашининаО. А.PashininaO. A.

Пашинина Ольга Александровна, к.м.н., руководитель научно-клинического отдела патологии уха и основания черепа

123182, Москва, Волоколамское шоссе, д. 30, корп. 2

Olga A. Pashinina, Cand. Sci. (Med.), Head of the Scientific and Clinical Department of Ear and Skull Base Pathology

30, Bldg. 2, Volokolamskoe Shosse, Moscow, 123182

OlgaP83@mail.ruhttps://orcid.org/0000-0002-9081-6016МихалевичА. Е.MikhalevichA. E.

Михалевич Антон Евгеньевич, к.м.н., старший научный сотрудник отдела патологии уха и основания черепа

123182, Москва, Волоколамское шоссе, д. 30, корп. 2

Anton E. Mikhalevich, Cand. Sci. (Med.), Senior Researcher of the Department of Pathology of the Ear and the Base of the Skull

30, Bldg. 2, Volokolamskoe Shosse, Moscow, 123182

Mikhalevichae@mail.ruhttps://orcid.org/0000-0002-5177-4255ПанинаО. С.PaninaO. S.

Панина Ольга Сергеевна, научный сотрудник отдела патологии уха и основания черепа

123182, Москва, Волоколамское шоссе, д. 30, корп. 2

Olga S. Panina, Researcher of the Department of Pathology of the Ear and the Base of the Sskull

30, Bldg. 2, Volokolamskoe Shosse, Moscow, 123182

dr.panina@gmail.comНациональный медицинский исследовательский центр оториноларингологииРоссияNational Medical Research Center for Otorhinolaryngology of the Federal Medico-Biological Agency of RussiaRussian Federation20221705202208150159Copyright © Диаб Х., Дайхес Н.А., Сайдулаев В.А., Юнусов А.С., Пашинина О.А., Михалевич А.Е., Панина О.С., 20222022Диаб Х., Дайхес Н.А., Сайдулаев В.А., Юнусов А.С., Пашинина О.А., Михалевич А.Е., Панина О.С.Diab K., Daikhes N.A., Saydulaev V.А., Yunusov A.S., Pashinina O.A., Mikhalevich A.E., Panina O.S.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.med-sovet.pro/jour/article/view/6882

Опухоль эндолимфатического мешка (ОЭМ) – редкое новообразование височной кости, гистологически является доброкачественным, но клинически ведет себя как злокачественное с деструкцией окружаю щих тканей. Опухоль исходит из области проекции эндолимфатического мешка, вызывает деструкцию задней поверхности каменистой части височной кости, структур внутреннего уха, сосцевидного отростка и т. д. ОЭМ может встречаться как спорадически, так и у больных с болезнью фон Гиппеля –Линдау. Из-за редкости этой опухоли ее легко спутать с другими опухолями, такими как параганглиома, аденома среднего уха, аденокарцинома, папиллярная карцинома щитовидной железы или папиллома сосудистого сплетения. Компьютерная томография (КТ) и магнитно-резонансная томография (МРТ) имеют важное диагностическое значение и играют большую роль при планировании тактики лечения. Оптимальным методом лечения является резекция патологически измененных тканей до здоровых. В некоторых случаях (неполное удаление опухоли с «положительными краями», пациенты с сопутствующими заболеваниями или неоперабельной опухолью) больные получают курсы рентген- или радиохирургии. При выявлении опухоли на ранних стадиях объем резекции может быть сведен к минимуму с сохранением слуха и вестибулярной функции внутреннего уха. Рецидив главным образом происходит из-за трудности определения границ опухоли и из-за обширной костной инфильтрации. Точный диагноз и правильное предоперационное планирование с эмболизацией, когда это возможно, облегчат оперативное вмешательство и позволят избежать осложнений из-за интраоперационного кровотечения. Длительное наблюдение важно для того, чтобы избежать рецидивов. Недостаточная освещенность данной проблемы в отечественной литературе связана с низким процентом ее встречаемости в отохирургической практике, что осложняет своевременную диагностику и лечение данного типа новообразований височной кости, ухудшает прогноз.

Endolymphatic sac tumors are rare neoplasms of the temporal bone, histologically benign, but clinically behaves as malignant tumors causing destruction of surrounding tissues. The tumor originates from the posterior surface of petrous part of temporal bone, where endolymphatic sac is situated anatomically. The tumor causes destruction of the posterior surface of the petrous part of the temporal bone, inner ear, mastoid process, etc. Endolymphatic sac tumor can be both sporadically and in patients with von Hippel – Lindau disease. Due to the rarity of this tumor, it is easy to confuse it with other tumors, such as paraganglioma, middle ear adenoma, adenocarcinoma, papillary thyroid carcinoma or papilloma of the vascular plexus. Computed tomography (CT) and magnetic resonance imaging (MRI) are of great diagnostic importance and play an important role in planning treatment tactics. The optimal method of treatment is resection of pathologically altered tissues. In some cases (incomplete resection of tumor, the patients with concomitant diseases or inoperable cases) receive courses of X-ray or radiosurgery. If a tumor is detected in the early stages, the volume of resection can be minimized while preserving hearing and vestibular function of the inner ear. Recurrence usually happens due to difficulty to identify the extension of the tumor. Diagnosis and correct preoperative planning, with embolization if it possible, will facilitate surgery and avoid subtotal tumor resection due to intraoperative bleeding. Long follow-up period is important in order to avoid recurrences. Insufficient coverage of this problem in the literature is associated with a low percentage of its occurrence in otosurgical practice, which complicates the timely diagnosis and treatment of this type of tumors of the temporal bone, worsens the prognosis.

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The authors declare that there are no conflicts of interest present.