A case of combined treatment of severe chronic thromboembolic pulmonary hypertension
https://doi.org/10.21518/2079-701X-2015-8-10-13
Abstract
Chronic thromboembolic pulmonary hypertension (CTEPH) is a rare disease which occurs in 1-3% of patients [2, 11] after pulmonary embolism. The incidence of CTEPH is 5-10 cases per 1 million population per year. Similar to other diseases associated with pulmonary hypertension (PH), CTEPH is malignant and has a poor prognosis. [4, 6, 8] There are a number of objective difficulties in the diagnosis of the disease: complaints and symptoms are very non-specific, there are often no X-ray aor ECG changes, echocardiographic signs of overload of right heart chambers are observed in the final stages of the disease. [9, 3] A strong inclination of doctors to primarily seek problems in the left heart chambers also plays a part in this. As a result, a patient may be visiting various specialists for years and receive treatment from different ailments including heart failure, asthma, pulmonary fibrosis, obstructive bronchitis. We had a case where a female patient with CTEPH received prednisolone for asthma for a long time while she had normal spirometry!
About the Authors
R. S. Akchurin
Russian Cardiology Research and Production Complex
Russian Federation
Russian Federation
I. E. Chazova
Russian Cardiology Research and Production Complex
Russian Federation
Russian Federation
K. V. Mershin
Russian Cardiology Research and Production Complex
Russian Federation
Russian Federation
T. V. Martynyuk
Russian Cardiology Research and Production Complex
Russian Federation
Russian Federation
T. V. Vdovenko
Russian Cardiology Research and Production Complex
Russian Federation
Russian Federation
N. M. Danilov
Russian Cardiology Research and Production Complex
Russian Federation
Russian Federation
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Review
For citations:
Akchurin RS, Chazova IE, Mershin KV, Martynyuk TV, Vdovenko TV, Danilov NM. A case of combined treatment of severe chronic thromboembolic pulmonary hypertension. Meditsinskiy sovet = Medical Council. 2015;(8):10-13. (In Russ.) https://doi.org/10.21518/2079-701X-2015-8-10-13
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